Dermatomyositis (DM) are systemic inflammatory disorders that
may be associated with diffuse interstitial lung disease.
Cause
The cause of dermatomyositis is unknown, but the disease has
much in common with autoimmune disorders, in which your immune
system mistakenly attacks your body tissues.
Genetic and environmental factors also might play a role.
Environmental factors could include viral infections, sun exposure,
certain medications and smoking.
SIGNS AND
SYMPTOMS
The signs and symptoms of dermatomyositis can appear suddenly or
develop gradually over time. The most common signs and symptoms
include:
- Skin changes. A violet-colored or dusky red
rash develops, most commonly on your face and eyelids and on your
knuckles, elbows, knees, chest and back. The rash, which can be
itchy and painful, is often the first sign of dermatomyositis.
- Muscle weakness. Progressive muscle weakness
involves the muscles closest to the trunk, such as those in your
hips, thighs, shoulders, upper arms and neck. The weakness affects
both the left and right sides of your body
Other symptoms are:
- muscle pain
- muscle tenderness
- problems swallowing
- lung problems
- hard calcium deposits underneath the skin, which is mostly seen
in children
- fatigue
- unintentional weight loss
- fever
- TREATMENT
Medications •
Corticosteroids •
Corticosteroid-sparing agents • Rituximab
(Rituxan) •Antimalarial medications. •Sunscreens
Therapy •Physical therapy •Speech therapy •Intravenous
immunoglobulin (IVIG) •surgery to remove calcium deposits