Question

1. The heart muscle cells prefer        as the primary energetic substrate.

A. Amino acids                       B. Fatty acids              C. Carbohydrates

2. Maple Syrup Urine disease is caused by?

A. Defects in phenylalanine catabolism                     B. Defects in catabolism of branched-chain amino acids

C. Defects in tyrosine catabolism

3. Which of the following hormones causes adipocytes to release fatty acids?

A. Insulin                    B. Glucagon

4. During starvation, the glycogens stored in the muscle contribute to the maintenance of blood glucose.

A. True                        B. False

Answer 1

1.

Fattyacid is the primary energetic substrate for heart muscle. Heart muscle also depends on substrate like glucose, pyruvate for energy production. Contraction of heart is needed for regular pumping of blood. This contraction requires energy. Main source of fuel for cardiac muscles are fatty acids.

2.

Mapple syrup urine disease is caused by defects in catabolism of branched chain amino acids.

Another name of mapple syrup urine disease is branched chain ketoaciduria. It occurs due to defect in catabolism of branched chain aminoacids like leucine, valine and isoleucine.

3.

Glucagon caused adipose tissue to release fatty acids. Glucagon having effects opposite to insulin. Glucagon having effect on adipose tissue. It enhance the lipolysis of triglycerides for the release of fatty acids. This helps in making fattyacids available for energy production.

4.

True.

Glycogen is the stored form of glucose in body. Glycogen is stored in liver and muscle tissue. At the time of starvation, glycogen stores in liver and muscle tissue breaks to form glucose.