In: Nursing
White Group CLC PPP:As a group, develop a 4 slide PowerPoint presentation
Cystic fibrosis
Include the following in the presentation:
A description of the impact of this disease or illness during childhood.
Evaluate how this disease or illness impacts the adult client in the following areas:
Susceptibility to engage in substance abuse.
Prenatal care and childbearing.
CYSTIC FIBROSIS: Cystic fibrosis is an inherited life-threatening and genetic disorder that damages the lungs and digestive system ( pancreas, liver, kidneys and intestine). it is an autosomal recessive disorder caused by the presence of mutations in both the copies of the gene. CYSTIC FIBROSIS IN CHILDHOOD: A child with cystic fibrosis has a faulty gene that affects the movement of sodium chloride in the cells. The resulted salty sweat and thickened digestive juices together can clog the lungs making the child to a) breathing difficulty b) lung infection and c) severe lung damage. In addition to this, absence of breakdown of thickened digestive fluids in the child's intestine results in digestive and growth problems. SIGNS AND SYMPTOMS IN CHILDREN: a) poor growth due to lack of digestive fluid breakdown and nutrients ansorption b) cough and wheezing c) salty sweat d) carving on foods with no weight gain and e) large, greasy stools. DIAGNOSTIC EVALUATION: A) Sweaty test ( In sweat test, a drug called Pilocarpine stimulant is used to spot on the arm to sweat and a piece of filter paper is used to absorb the areato fid out sodium or chloride.) B) A famly history of cystic fibrosis C) Chest X-ray and D) Genetic tests ( blood or saliva). TREATMENT: a) ANTIBIOTICS: Symptoms vary from child to child and need ongoing medical care to those who are affected. The sputum and mucus should be taken frequently to find out the cause or germs that causing lung infection. Antibiotics should be given intravenously for children if the symptoms flare up. B) VACCIANTION: If the child is diagnosed with cystic fibrosis, the child should receive routine childhood vaccination along with other vaccines. C) Proper nutrition: To overcome poor growth due to lack of digestion and absorption, the parents should take care of their child with adequate nutritional supply to make them strong, healthier and well nourished. SUSCEPTIBILITY TO ENGAGE IN SUBSTANCE ABUSE ( ADULTS) : Substance abuse more commonly associated with anxiety and depression followed by misuse of substances such as alcohol, tobacco and illegal drugs. This usage of tobacco and illegal drugs are harmful to people with cystic fibrosis and should be avoided to prevent from lung infection and also from exposure to second hand smoke.In addition to this, too much of alcohol usage can also damage the liver and affects the immune system and prone to get infections. Moreover, people with cystic fibrosis often feel pain and physicians prescribes medicines to reduce pain. In such cases of drug abuse, the patients takes the medications more frequently than prescribed that produces a negative impact on the health satusof the patient with cystic fibrosis. PRENATAL CARE AND CHILD BEARING IN ADULTS WITH CYSTIC FIBROSIS: Women with mild cystic fibrosis have little difficulty in childbearing due to dehydrated cervical mucus. Physicians should instruct the child bearing women to increase emphasis on controlling pulmonary infection and should get adequate nutrition. They should also avoid teratogenic drugs and with no proven record.