Question

1- Cite one example of an inborn error of metabolism and describe the best nutrition-related intervention.

2- ID two healthy outcomes related to successful treatment for polycystic ovary disease.

3- Give an example of an approved supplement claim that may appear on the label ( “Supplement Facts” panel)

Answer 1

1) Inborn error of metabolism form a large class of genetic diseases involving congenital disorders of metabolism. The majority are the defects in the single genes ,also called as Congenital Metabolic diseases or Inherited Metabolic disease..There are many disorders classified . Lets see how dietary management is done for Amino acid disorder of metabolism.

Eg Phenylketonuria:

It is the result of decreased metabolism of amino acid phenoalanine.

The nutrition related intervention for this problem can be tackled well by including the following food

• Starch food (Potatoes, corn)
• Low protein diet
• Fruits
• Vegetables

Foods to avoid:

Soybeans, egg white,shrimp,chicken breast, spirulina,fish, nuts ,cray fish, lobster,tuna, turkey,legumes, low fat cottage cheese

2)Successful treatment for Polycystic Ovary Disease:

Dietary modification should include the following

• Low GI diet (whole fruit , vegetables,whole grains, lean protein. healthy fats, processed refined carbs, low diary products
• Regular excercise may improve insulin resistance and ovulation ,help burn body fat and reduce inflammatory markers
• High Protein diet will reduce appetite
• decrease the carbhohydrate foods

3) Supplemental Facts :

The supplemental fact panel includes the amount of calories , Carbhohydrate,Protein ,Vitamins, Minerals , fats and water. This shold be approved by the FDA

Eg . Health dirinks like Horlicks, Boost Bournvita, Maltova,Vivo ,Complan

This are approved with the following

• calories
• carbs and sugars
• Protein
• Fats
• Vitamin A
• Vitamin C
• Calcium
• Iron